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Ciliary Dyskinesia

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September 21, 2023
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Idrevloride in hypertonic saline improves lung function in primary ciliary dyskinesia

Idrevloride in combination with hypertonic saline for 28 days resulted in better lung function vs. hypertonic saline alone in primary ciliary dyskinesia, according to a European Respiratory Society International Congress presentation.

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July 19, 2023
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Airway disease on CT differs based on primary ciliary dyskinesia defect type

On chest CTs, children with primary ciliary dyskinesia and inner dynein arm/microtubular disorganization defects had more mucus plugging than other defects, according to results published in Annals of the American Thoracic Society.

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April 03, 2023
3 min read
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Airway inflammation linked to impaired lung function in primary ciliary dyskinesia

High sputum inflammatory concentrations in children with primary ciliary dyskinesia were linked to high structural lung injury percentages, according to study results published in Annals of the American Thoracic Society.