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Romano-Ward Syndrome
Romano-Ward syndrome is a genetic condition associated with a prolonged QT interval on the ECG.
Unlike Jervell-Lange-Nielsen, there is no congenital hearing loss present in Romano-Ward syndrome.
A mutation of the cardiac potassium channel or sodium channel is responsible and can be from one of multiple genetic mutations relating to these channels. Treatment includes beta-blockers, however if syncope or sustained ventricular arrhythmias are present, an implantable cardioverter defibrillator (ICD) is indicated to prevent sudden cardiac death.
